Pulmonary capillary hemangiomatosis: an unusual cause of primary pulmonary hypertension in pediatric age group

Pulmonary capillary hemangiomatosis (PCH) is a rare and controversial entity that known to be cause of pulmonary hypertension microscopically characterized by proliferation dilated capillary-sized channels along in the alveolar walls. Clinically, it mostly seen adults. PCH’s main clinical presentations are progressive dyspnea, fatigue, hemoptysis, palpitations later irreversible right-sid­ed heart failure. It severe hypoxemia, centrilobular ground-glass opacities on computed tomography congestion triggered vasodilating therapy. The imaging features include diffuse ground‑glass with hypertension. We present case PCH 4‑year‑old boy who was diagnosed post-partum hemorrhage (PPH) echocardiography thorax.